View Product Catalogue

Search our database to view details of all our products.

More Details

View our Recipes

Click here to view our nutritional recipes

More Details

Latest news

CASE STUDY: Intensive Nutritional Intervention in a Frail, Elderly Patient

David Gray, Senior Specialist Dietitian at Guy’s and St Thomas’…

Case Study - Post-Pyloric feeding in gastroparesis: the role of high protein enteral feeds

Michelle Barry, Specialist Home Enteral Feeding Dietitian

There are several…

Available 1st March: 3 New Fortisip 2kcal Flavours

Help support your patients recovery with three tasty new flavours…

Nutricia Suggestion Engine - Conditions

Step 1

What information would you like to see?


Step 2

In order to show you information relevant to you, please select a condition of interest.

Step 3

Press the 'find' button below to find relevant articles,videos and podcasts.

You are viewing Consumer Information

PKU (Phenylketonuria)

Phenylketonuria (or PKU as it is commonly called) is an inherited (autosomal) disorder of phenylalanine metabolism, caused by a deficiency of the enzyme phenylalanine hydroxylase. It is the most common Hyperphenylalaninemia and can be classified into 3 groups:

* Classical Phenylketonuria (PKU), where the dietary tolerance to Phe is less than 350-400 mg per day and then residual activity of PAH is less than 5%.
* Moderate or Mild Phenylketonuria (PKU), dietary tolerance to Phe is less than 350-600 mg per day and then residual activity of PAH is less than 10%.
* Benign Phenylketonuria (PKU), where there are no dietary restrictions of Phe but the residual activity of PAH is less than 5%.

People with this condition will lead normal lives as long as they follow their prescribed treatments.

HCP Information for PKU (Phenylketonuria)

The content provided by Nutricia is for information purposes only and is in no way intended to be a substitute for medical consultation with your doctor, dietitian or healthcare professional. The information, opinions, and recommendations presented in these pages are not intended to replace the care of your own doctor, dietitian or healthcare professional. Before you make any changes in the management of your diet / treatment or any other persons diet /treatment you should always consult your doctor, dietitian or healthcare professional. Although we carefully review our content, Nutricia cannot guarantee or take responsibility for the medical accuracy of documents we publish, nor can Nutricia assume any liability for the content of any web site linked to our site. © 2016 Nutricia. All rights reserved.